Rare Occurrence of Paratesticular Rhabdomyosarcoma in Adulthood: A Case Report

Mohammad Hifzi Mohd Hashim, Zulkifli Md Zainuddin, Khoo Hau Chun, Li Yi Lim, Gilbert Peh Voon Yeow

Abstract


Paratesticular rhabdomyosarcoma is an extremely rare malignant tumour that primarily affects pediatric patients but is uncommon in adults. Prompt diagnosis and treatment are essential to prevent metastasis and improve prognosis. A 28-year-old male was presented with a painless right scrotal swelling. Physical examination revealed a palpable mass in the right scrotal region, raising suspicion of a malignant tumour. Ultrasonography showed a hypoechoic mass originating from the right epididymis. The patient underwent a high inguinal orchidectomy, and histopathological examination confirmed the diagnosis of paratesticular rhabdomyosarcoma. Staging computed tomography revealed no evidence of metastasis. The patient received chemotherapy based on risk stratification. Paratesticular rhabdomyosarcoma carries a poor prognosis in advanced stages, highlighting the importance of early diagnosis. Surgery remains the mainstay of treatment and the role of adjuvant therapy in adults is not well established. Understanding the clinical manifestations, diagnosis and treatment of this rare malignancy can aid in improved management and outcomes

Keywords


Adolescent; chemotherapy; orchidectomy; paratesticular; rhabdomyosarcoma

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References


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DOI: http://dx.doi.org/10.17576//JSA.2024.1402.02

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